Table 1 of
Zhou, Mol Vis 2012; 18:1379-1383.
Table 1. Clinical features of patients with Usher syndrome type I
Patient | Age | Vision | Refraction | Visual field | Fundus |
---|---|---|---|---|---|
II-1 | 18 | OD:20/25 | Plano | Nasal loss | Optic nerve head drusen |
OS:20/25 | Plano | Nasal loss | Optic nerve head drusen | ||
II-2 | 10 | OD:20/40 | −4.50+0.50×100 | Nasal loss | See Figure 3 |
OS:20/50 | −4.50+0.50×100 | Nasal loss | See Figure 3 | ||
II-3 | 13 | OD:20/25 | −1.00+1.75×95 | See Figure 2 | Bone spicules |
OS:20/50 | −1.50+1.50×43 | See Figure 2 | Bone spicules | ||
II-4 | 9 | OD:20/50 | −0.50+2.00×80 | Nasal loss | Bone spicules |
OS:20/200 | −0.50+1.75×83 | Nasal loss | Bone spicules |