Table 1 of Zhou, Mol Vis 2012; 18:1379-1383.


Table 1. Clinical features of patients with Usher syndrome type I

Patient Age Vision Refraction Visual field Fundus
II-1 18 OD:20/25 Plano Nasal loss Optic nerve head drusen
    OS:20/25 Plano Nasal loss Optic nerve head drusen
II-2 10 OD:20/40 −4.50+0.50×100 Nasal loss See Figure 3
    OS:20/50 −4.50+0.50×100 Nasal loss See Figure 3
II-3 13 OD:20/25 −1.00+1.75×95 See Figure 2 Bone spicules
    OS:20/50 −1.50+1.50×43 See Figure 2 Bone spicules
II-4 9 OD:20/50 −0.50+2.00×80 Nasal loss Bone spicules
    OS:20/200 −0.50+1.75×83 Nasal loss Bone spicules