Figure 2. Sclerocornea. This is a case of sclerocornea, i.e., peripheral scleralization of the cornea, accompanied by the feature of
cornea plana (CNA2, OMIM
217300) which in this review we designate S-CNA to distinguish it from total corneal opacification (S-CCO, see
Figure 3A,B). In S-CNA the anterior segment is otherwise normal.