Figure 3. Total corneal opacification. Two typical examples of the phenotype designated as total congenital corneal opacification. S-CCO (A-D). This condition confusingly, has been previously described clinically as sclerocornea in the literature. However, anterior segment imaging using UBM shows that the lens has failed to form normally in case A and B and that in case C and D there is failure of the lens (L) to separate from the cornea (ILA) and there is an abnormal zonular ciliary complex (Z); this suggests another primary lens problem leading to a secondary CCO. Note both opacities are vascularized.