Figure 3. Three probands with the KIF11 mutation c.2153A>T (p. H718L) present as entirely unilateral familiar exudative vitreoretinopathy. A, B: The right eye is healthy, and the left eye presents as total retinal detachment with shallow anterior chamber in a 1-month old girl. C, D: Proband 4: The right eye of a 1-year old boy shows retinal fold with proliferation and exudation. The left eye is normal. E, F: Proband 9: The fundus images of a 7-year-old boy show that the right eye is normal, and a falciform retinal fold is observed in the left eye. G, H: Proband 7: During follow-up, the retinal fold progressed to exudative retinal detachment gradually in the left eye of Proband 7. OD and OS represent the right and left eye, respectively.