Table 4 of
Maeda-Katahira, Mol Vis 2019; 25:559-573. Table 4 of
Maeda-Katahira, Mol Vis 2019; 25:559-573.
Table 4. Auditory findings of four patients with DOA-plus phenotype.
| Case | Age of onset | Chief complaint | Audiometric tests | Maximum speech discrimination scores | DPOAE | ABR |
|---|---|---|---|---|---|---|
| 1 | 17 | Hearing impairment | A bilateral sensorineural hearing loss of approximately 20–40 dB | 45% in right ear, 20% in left ear | Normal | Absent bilaterally |
| 2 | 15 | Hearing impairment | A bilateral sensorineural hearing loss of approximately 60 dB | 20% in both ears | Normal | Absent bilaterally |
| 3 | 16 | Hearing impairment | A bilateral sensorineural hearing loss of approximately 50 dB in right, and 40 dB in left | 40% in right ear, 30% in left ear | Normal | Absent bilaterally |
| 4 | 16 | Hearing impairment | A bilateral sensorineural hearing loss of approximately 70 dB in right, and 60 dB in left | 0% in both ears | Normal | Absent bilaterally |