Table 1 of Jiang, Mol Vis 2013; 19:418-423.
BPES families | Subtype | Affected individuals | Age (years) | IICD (mm) | IPFH (mm) | HPFL (mm) | Levator function (mm) | Surgical stages (preoperatively) | |||
---|---|---|---|---|---|---|---|---|---|---|---|
RE | LE | RE | LE | RE | LE | ||||||
family A | II | III:1 | 47 | 38 | 2 | 3 | 22 | 22 | 2 | 2 | Stage 1 |
family B | unknown | II:3 | 50 | 39 | 3 | 3 | 21 | 21 | 2 | 2 | Stage 1 |
family C | II | II:1 | 63 | 36 | 4 | 4 | 23 | 23 | 2 | 2 | Stage 2 |