Molecular Vision: Fujinami, Mol Vis 2013; 19:1580-1590. Table 3

Table 3. Electrophysiological Findings of Four Japanese Patients with KCNV2-retionpathy

Pt	DA 0.01		DA 30.0				Square shaped a-wave	Excessive enlargement of b-wave in the extended protocol	LA 3.0			LA 3.0 30Hz
	Amp (μv)	PT (ms)	A-wave		B-wave				A-wave	B-wave		B-wave
	Amp (μv)	PT (ms)	Amp	PT	Amp	PT			Amp	PT	Amp	PT	Amp	PT
1	N	Del	N	Del	Super N	NA	(+)	(+)	Sub N	Del	Sub N	UD	UD	UD
2	UD	UD	N	Del	Super N	NA	(+)	NA	Sub N	Del	Sub N	Del	Sub N	Del
3	Sub N	Del	N	Del	Super N	N	(+)	NA	Sub N	Del	Sub N	Del	Sub N	N
4	Sub N	Del	N	Del	Super N	NA	(+)	(+)	Sub N	Del	Sub N	Del	Sub N	Del

Pt = patient; Amp = amplitude; PT = peak time; N = normal; UD = undetectable response; Sub N = subnormal; Del = delayed response; Super N=supernormal response; NA = not available. Full-field electroretinography (ERG) incorporating the standards of the International Society for Clinical Electrophysiology of Vision (ISCEV) included: (i) dark adapted dim flash 0.01 cd•s•m^-2 (DA0.01), (ii) dark adapted bright flash 30.0 cd•s•m^-2 (DA30.0), (iii) light adapted 3.0 cd•s•m^-2 at 2 Hz (LA 3.0), and (iv) light adapted 3.0 cd•s•m^-2 30 Hz flicker (LA 3.0 30 Hz). The extended protocol also included the recording of dark adapted responses to an intensity series of flashes in order to detect an excessive enlargement of dark adapted b-wave (patients 1 and 4).