Figure 2. Electrophysiological findings of each patient with potassium channel, subfamily V, member 2 (KCNV2) retinopathy. Full-field electroretinograms (ERGs) of patient 1 (top row), patient 2 (second row), patient 3 (third row), and patient 4 (forth row) are shown. The ERGs from a normal control (bottom row) are also shown for comparison. All four patients underwent full-field ERG testing with the minimum standards of the International Society for Clinical Electrophysiology of Vision (ISCEV): (i) dark adapted dim flash 0.01 cd•s•m⁻² (DA 0.01), (ii) dark adapted bright flash 30.0 cd•s•m⁻² (DA 30.0), (iii) light adapted 3.0 cd•s•m⁻² at 2 Hz (LA 3.0), and (iv) light adapted 3.0 cd•s•m⁻² 30 Hz flicker ERG (LA 3.0 30Hz). The extended protocol was applied to two subjects (patients 1 and 4), including the recording of dark-adapted ERGs to an intensity series of flashes; 0.001 cd•s•m-², 0.01 cd•s•m⁻², 0.3 cd•s•m⁻², 3.0 cd•s•m⁻², and 30.0 cd•s•m⁻².