Table 3 of Xu, Mol Vis 2012; 18:3021-3028.


Table 3. Functional data.

Family/patient OCT Visual field Full field ERG (photopic and scotopic)
ADRP-HT/III:1 Preserved foveal lamination, disappearance of IS/OS layer in periphery 10° both horizontally and vertically Non-recordable
ADRP-LG/III:9 Preserved foveal lamination, disappearance of IS/OS layer in periphery 10° both horizontally and vertically Only residual cone responses
ADRP-LLN/III:1 Preserved foveal lamination, disappearance of IS/OS layer in periphery Tunnel vision, <5° both horizontally and vertically non-recordable in scotopic ERG and the cone responses were markedly reduced
ADRP-XL/IV:1 Preserved foveal lamination, disappearance of IS/OS layer in periphery Tunnel vision, <5° both horizontally and vertically, more severe in the left eye Non-recordable