Figure 2. Fundus photos of three patients and a normal control. II:2 and II:7 demonstrated the typical macular atrophy observed in the six adult patients. III:1 at two and half years old showed mild granular retinal pigment epithelial changes, with the tiny yellowish-white deposits in the macula observed in the two youngest patients. Temporal pallor of the optic disc was observed in patients II:2, II:7, and III:1. Mild artery attenuation was noticed in II:2 and II:7. Ctr: fundus photo of a normal control.