Figure 3. Family 2: two affected
brothers. A: At six years of age, the proband developed
right acute pupillary block glaucoma. Complete crystalline lens
dislocation into the anterior chamber of the right eye can be
seen. In the left eye, inferotemporal crystalline lens
subluxation can be appreciated. Both corneas are symmetrically
enlarged (14 mm horizontal diameter). B, C: The
proband's brother had lens-related pupillary block glaucoma in
the left eye for which he had bilateral lensectomy and anterior
vitrectomy at four years of age. At ten years of age,
glaucomatous cupping in the left eye (C) as opposed to
the right eye (B) can be appreciated. Megalocornea (not
shown) was symmetric (14 mm horizontal corneal diameters without
scars or breaks).