Table 3 of Xu, Mol Vis 2011; 17:1537-1552.


Table 3. Clinical features of the probands from the four Chinese families with retinitis pigmentosa (RP) or Usher syndrome type II (USH2)




Family
number




Proband
Best
corrected
visual
acuity
(R/L)
Oneset
age of
night
blindness
(year)



Fundus
appearance
Oneset
age of
hearing
loss
(year)



Hearing
impairment




Cataract



Visual
field




ERG



Vestibular
function
FR1 077006 0.4/0.4 25 RP Normal hearing Normal Both eyes N/A Wave undetectable Normal
F6 073001 0.5/0.4 13 RP 5 Moderate(sp) No N/A N/A Normal
F7 019082 1.0/1.0 17 RP 1 Moderate(sp) No 10° N/A Normal
F8 019092 0.6/0.6 12 RP 8 Moderate(sp) No 10–15° Wave undetectable Normal