Table 1 of Liu, Mol Vis 2010; 16:454-461.
Patient number |
Age (year) |
Best corrected visual activity (R/L) |
Fundus appearance |
Hearing impairment |
ERG |
Vestibular function |
---|---|---|---|---|---|---|
III:1 | 55 | FC/FC | RP | Mild | extinct | normal |
III:3 | 53 | FC/HM | RP | Mild | extinct | normal |
III:5 | 47 | FC/FC | RP | Mild | extinct | normal |
IV:1 | 25 | 0.15/0.1 | RP | Normal | N/A | normal |
IV:2 | 19 | 0.6/0.6 | RP | N/A | N/A | normal |