Figure 1. Ocular findings in a Korean XLRS patient (case 16). A: Fundus photograph of the both eyes showed typical stellate pattern of schisis cavities in the macula. The inset presents an image of the macula magnified twofold. B: Fluorescein angiogram showed no definite leakage from the cystic cavities. C: Optical coherence tomography showed the schisis in the nerve fiber layer. D: Electroretinogram showed markedly decreased amplitude of b-wave and relative preservation of a-wave, which are key features of XLRS.