Table 1 of Romero, Mol Vis 2008; 14:829-835.


Table 1. Clinical features in the affected and unaffected family members.






Best-corrected vision




Case Age Gender Status Age of onset OD OS Corneal lesions Synchronic Symmetry Degree* Degree**
II-1 73 F Affected 37

Yes#



II-3 69 M Affected 42 0.13 0.13 Yes Yes No Bad 4
II-4 68 F Not affected - 1 1




III-2 55 M Affected 17

Yes##



III-4 42 M Not affected - 1 1




III-5 44 F Affected 30 0.28 0.13 Yes No Yes Bad 4
III-6 40 F Affected 28 0.5 0.4 Yes Yes Yes Intermediate 3
III-7 43 M Not affected - 1 1




IV-2 16 F Affected 5






IV-3 15 M Affected 3 1 1 Yes Yes Yes Very good 1
IV-4 15 F Affected 4 1 1 Yes Yes Yes Very good 1
IV-5 8 M Affected 4 0.5 0.67 Yes Yes No Good 2