Table 1 of Romero, Mol Vis 2008; 14:829-835.
Table 1. Clinical features in the affected and unaffected family members.
Best-corrected vision | |||||||||||
Case | Age | Gender | Status | Age of onset | OD | OS | Corneal lesions | Synchronic | Symmetry | Degree* | Degree** |
II-1 | 73 | F | Affected | 37 | Yes# | ||||||
II-3 | 69 | M | Affected | 42 | 0.13 | 0.13 | Yes | Yes | No | Bad | 4 |
II-4 | 68 | F | Not affected | - | 1 | 1 | |||||
III-2 | 55 | M | Affected | 17 | Yes## | ||||||
III-4 | 42 | M | Not affected | - | 1 | 1 | |||||
III-5 | 44 | F | Affected | 30 | 0.28 | 0.13 | Yes | No | Yes | Bad | 4 |
III-6 | 40 | F | Affected | 28 | 0.5 | 0.4 | Yes | Yes | Yes | Intermediate | 3 |
III-7 | 43 | M | Not affected | - | 1 | 1 | |||||
IV-2 | 16 | F | Affected | 5 | |||||||
IV-3 | 15 | M | Affected | 3 | 1 | 1 | Yes | Yes | Yes | Very good | 1 |
IV-4 | 15 | F | Affected | 4 | 1 | 1 | Yes | Yes | Yes | Very good | 1 |
IV-5 | 8 | M | Affected | 4 | 0.5 | 0.67 | Yes | Yes | No | Good | 2 |