Molecular Vision: Xie, Mol Vis 2008; 14:1666-1672. Table 2

Table 2. Clinical appearance of the affected members

Family member	Sex	Age (years)	Age of onset (years)	Visual acuity	Maximum IOP (mmHg)	Cup-disc ratio	VF grading score	Severity	Medical therapy
III:1	M	66	23	OD: NLP	46	**	#	End stage	Surgery##
				OS: NLP	44	**	#	End stage	Surgery
III:3	F	63	24	OD: NLP	*	**	#	End stage	Surgery
				OS: NLP	*	**	#	End stage	Surgery
III:8	F	56	26	OD: NLP	*	**	#	End stage	Surgery##
				OS: NLP	*	**	#	End stage	Surgery
III:14	F	38	21	OD: NLP	*	**	#	End stage	Surgery
				OS: NLP	*	**	#	End stage	Surgery
III:15	M	35	19	OD: NLP	*	**	#	End stage	Surgery
				OS: NLP	*	**	#	End stage	Surgery
IV:2	F	42	41	OD: 0.5	28	0.7	1	Mild	No
				OS: 0.4	22	0.6	2	Mild	No
IV:4	M	36	26	OD: NLP	*	**	#	End stage	Surgery
				OS: NLP	*	**	#	End stage	Surgery
IV:10	M	30	22	OD:0.01	29	1	8	Severe	Surgery
				OS: NLP	28	1	#	End stage	Surgery
IV:14	M	40	16	OD: NLP	29	0.8	#	End stage	No
				OS: NLP	32	0.8	#	End stage	No
IV:20	M	33	26	OD: NLP	28	**	#	End stage	No
				OS: NLP	*	**	#	End stage	Surgery
IV:22	M	35	30	OD: 1.0	18	0.4	0	Mild	No
				OS: 0.25	35	0.6	3	Moderate	No

The asterisk indicates that the maximum intraocular pressure (IOP) was not certain because of relatively advanced glaucoma at the time of first presentation. The double asterisk indicate that the cup/disc ratio was not certain because of eyeball atrophy or cornea opacity. The sharp (hash mark) indicates that the visual field was not available because the patient had no light perception. The double sharp (hash marks) indicates that the member had surgery twice. The visual fields (VF) were graded for severity of visual field loss with a level grading scale. Severity classification is leveled by the visual field score: mild (0–2), moderate (3–5), severe (6–8), and end stage (no light perception). NLP, no light perception.