Table 4 of Zhuo, Mol Vis 2008; 14:1533-1539.


Table 4. Phenotype characteristic of the 17 patients with JOAG from GZ.1 pedigree at last follow up.


Subject
number


Age


Gender
BCVA IOP (mmHg) C/D VF

RE

LE

RE

LE
RE LE
RE

LE
V H V H
II2 74 F 0.3 NLP 17.1 17.5 0.8 0.8 0.9 0.9 N/A N/A
II4 65 F 0.3 0.5 7 22.6 0.6 0.7 0.9 0.8 PC IZD
II6 58 F 1.0 1.2 15.6 12.1 0.4 0.5 0.6 0.7 N/A N/A
III1 59 F 0.4 0.7 16.3 13.7 0.9 0.8 0.9 0.8 N/A N/A
III4 48 F 1.5 1.2 27.3 23 0.5 0.5 0.7 0.7 N N
III5 44 M LP 1.2 19 18 1.0 1.0 0.8 0.7 N/A N/A
III7 38 F 1.5 0.1 14 15.4 0.4 0.4 1.0 0.9 N/A N/A
III8 55 F 1.0 0.6 13 16 0.5 0.6 0.95 0.85 N/A N/A
III19 35 M 1.5 1.2 15.2 17.9 0.2 0.2 0.2 0.2 N/A N/A
IV1 37 M 0.1 LP 16 19 0.9 1.0 1.0 1.0 N/A N/A
IV2 36 M 1.5 1.5 14 19 0.2 0.2 0.4 0.5 N/A N/A
IV8 26 F 1.0 1.2 11 19 1.0 1.0 0.9 0.9 IZD IZD
IV9 21 F 1.5 1.5 28 26 0.3 0.4 0.5 0.5 N N
IV10 19 M 1.5 1.2 36 37 0.9 0.8 0.55 0.6 IZD N
IV11 18 M 1.5 HM 8 7 0.5 0.4 0.3 0.3 N/A N/A
IV16 31 F 1.0 0.9 10 16 0.5 0.5 1.0 1.0 N/A N/A
IV17 32 M 0.5 0.6 8 8 0.8 0.8 0.8 0.8 N/A N/A