Figure 3. Clinical optical features of pseudoxanthoma elasticum. 141514The retina of the right eye of case 5 shows peau d'orange (diffuse, mottled hyperpigmentation) and angioid streaks, as indicated by arrows. The angioid streaks resemble retinal blood vessels and radiate from the optic disc to the periphery of the retina. These two signs are the most frequent ophthalmologic features of pseudoxanthoma elasticum.