Figure 2. Fundus photographs before and after dark adaptation

Fundus photographs from two carriers (numbers 9 and 14) and three patients (numbers 11, 13, and 15) taken under ordinary light and after 4 h of dark adaptation (DA). The number on lower left corner represents the individual identification number as shown in pedigree on Figure 4. Photos with an asterisk (*) on the lower right corner were taken immediately after 4 h of dark adaptation. Generalized carpet-like retinal degeneration on the peripheral retina before (top left) and after (top right) 4 h of dark adaptation. Such peripheral retinal changes presented in all three affected individuals. A silver-gray or golden-yellow metallic sheen of the fundus or retinal vessels standing out in relief against a radiant background was not obvious in any of the patients. There were no obvious changes of color after 4 h of dark adaptation in affected individuals number 11 or 15.