Table 1 of
Kumar, Mol Vis 2004;
10:399-402.
Table 1. Clinical descriptions of patients
This table provides the age of onset of RP, BCVA, refraction and visual field data for all seven affected individuals. The best corrected Snellen visual acuity is abbreviated "BCVA"; light perception vision is abbreviated "LP".
Age now Patient (age at onset) Eye BCVA Refraction Visual field ------- -------------- --- ---- ------------------------ ------------- III-4 52 (-) OU LP N/A N/A IV-1 23 (18) OD 6/24 +0.5 x -1.5 40° (6/24) Tunnel vision OS 6/36 +0.5 x -1.5 140° (6/36) Tunnel vision IV-2 20 (15) OD 6/18 -4.0 x -1.0 20° (6/18) Tunnel vision OS 6/18 -4.5 x -1.0 110° (6/18) Tunnel vision IV-3 18 (12) OD 6/12 -8.0 x -3.0 50° (6/12) Tunnel vision OS 6/18 -8.0 x -2.5 140° (6/18) Tunnel vision IV-4 13 (10) OD 6/24 -3.0 x -2.0 20° (6/36) Tunnel vision OS 6/18 -3.0 x -2.0 160° (6/18) Tunnel vision IV-5 11 (8) OD 6/9 -8.0 (6/9) Tunnel vision OS 6/9 -8.0 (6/9) Tunnel vision IV-7 16 (11) OD 6/36 -2.75 (6/36) Tunnel vision OS 6/18 -1.0 x -1.0 180° (6/18) N12 |