Table 1 of
Kumar, Mol Vis 2004;
10:399-402.
Table 1. Clinical descriptions of patients
This table provides the age of onset of RP, BCVA, refraction and visual field data for all seven affected individuals. The best corrected Snellen visual acuity is abbreviated "BCVA"; light perception vision is abbreviated "LP".
Age now
Patient (age at onset) Eye BCVA Refraction Visual field
------- -------------- --- ---- ------------------------ -------------
III-4 52 (-) OU LP N/A N/A
IV-1 23 (18) OD 6/24 +0.5 x -1.5 40° (6/24) Tunnel vision
OS 6/36 +0.5 x -1.5 140° (6/36) Tunnel vision
IV-2 20 (15) OD 6/18 -4.0 x -1.0 20° (6/18) Tunnel vision
OS 6/18 -4.5 x -1.0 110° (6/18) Tunnel vision
IV-3 18 (12) OD 6/12 -8.0 x -3.0 50° (6/12) Tunnel vision
OS 6/18 -8.0 x -2.5 140° (6/18) Tunnel vision
IV-4 13 (10) OD 6/24 -3.0 x -2.0 20° (6/36) Tunnel vision
OS 6/18 -3.0 x -2.0 160° (6/18) Tunnel vision
IV-5 11 (8) OD 6/9 -8.0 (6/9) Tunnel vision
OS 6/9 -8.0 (6/9) Tunnel vision
IV-7 16 (11) OD 6/36 -2.75 (6/36) Tunnel vision
OS 6/18 -1.0 x -1.0 180° (6/18) N12
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