Table 1 of Kumar, Mol Vis 2004; 10:399-402.


Table 1. Clinical descriptions of patients

This table provides the age of onset of RP, BCVA, refraction and visual field data for all seven affected individuals. The best corrected Snellen visual acuity is abbreviated "BCVA"; light perception vision is abbreviated "LP".

             Age now
Patient   (age at onset)   Eye   BCVA          Refraction          Visual field
-------   --------------   ---   ----   ------------------------   -------------

 III-4       52  (-)       OU     LP    N/A                        N/A

  IV-1       23 (18)       OD    6/24   +0.5 x -1.5 40°   (6/24)   Tunnel vision
                           OS    6/36   +0.5 x -1.5 140°  (6/36)   Tunnel vision

  IV-2       20 (15)       OD    6/18   -4.0 x -1.0 20°   (6/18)   Tunnel vision
                           OS    6/18   -4.5 x -1.0 110°  (6/18)   Tunnel vision

  IV-3       18 (12)       OD    6/12   -8.0 x -3.0 50°   (6/12)   Tunnel vision
                           OS    6/18   -8.0 x -2.5 140°  (6/18)   Tunnel vision

  IV-4       13 (10)       OD    6/24   -3.0 x -2.0 20°   (6/36)   Tunnel vision
                           OS    6/18   -3.0 x -2.0 160°  (6/18)   Tunnel vision

  IV-5       11  (8)       OD    6/9    -8.0              (6/9)    Tunnel vision
                           OS    6/9    -8.0              (6/9)    Tunnel vision

  IV-7       16 (11)       OD    6/36   -2.75             (6/36)   Tunnel vision
                           OS    6/18   -1.0 x -1.0 180°  (6/18)   N12

Kumar, Mol Vis 2004; 10:399-402 <http://www.molvis.org/molvis/v10/a50/>
©2004 Molecular Vision <http://www.molvis.org/molvis/>
ISSN 1090-0535